Sotatercept for the Treatment of Pulmonary Arterial Hypertension.
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Pulmonary Arterial Hypertension and Hereditary Haemorrhagic Telangiectasia.
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Int J Mol Sci. 2018 Oct 17;19(10):3203. doi: 10.3390/ijms19103203.
Hereditary pulmonary arterial hypertension burden in pediatrics: A single referral center experience.
Ishizuka M, Zou W, Whalen E, Ely E, Coleman RD, Lopez-Terrada DH, Penny DJ, Fan Y, Varghese NP.
Front Pediatr. 2023 Mar 29;11:1050706. doi: 10.3389/fped.2023.1050706. eCollection 2023.
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Matsubara H, Ogawa A.
J Cardiol. 2014 Oct;64(4):243-9. doi: 10.1016/j.jjcc.2014.06.009. Epub 2014 Jul 28.
Single-Cell Imaging Maps Inflammatory Cell Subsets to Pulmonary Arterial Hypertension Vasculopathy.
Ferrian S, Cao A, McCaffrey EF, Saito T, Greenwald NF, Nicolls MR, Bruce T, Zamanian RT, Del Rosario P, Rabinovitch M, Angelo M.
Am J Respir Crit Care Med. 2024 Jan 15;209(2):206-218. doi: 10.1164/rccm.202209-1761OC.
Case report: Pulmonary arterial hypertension in ENG-related hereditary hemorrhagic telangiectasia.
Liu D, Xu F, Gao Q, Zhai Z.
Front Cardiovasc Med. 2022 Nov 10;9:1020762. doi: 10.3389/fcvm.2022.1020762. eCollection 2022.
Effect of Transcriptional Regulator ID3 on Pulmonary Arterial Hypertension and Hereditary Hemorrhagic Telangiectasia.
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Int J Vasc Med. 2019 Jul 11;2019:2123906. doi: 10.1155/2019/2123906. eCollection 2019.
Pulmonary arterial hypertension in hereditary hemorrhagic telangiectasia associated with ACVRL1 mutation: a case report.
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J Med Case Rep. 2022 Mar 1;16(1):99. doi: 10.1186/s13256-022-03296-9.
Pulmonary hypertension in hereditary hemorrhagic telangiectasia: A clinical review.
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Pulm Circ. 2023 Oct 19;13(4):e12301. doi: 10.1002/pul2.12301. eCollection 2023 Oct.
Defining the clinical validity of genes reported to cause pulmonary arterial hypertension.
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